565 Gorlin Syndrome: A Case of Recurrence of Odontogenic Keratocysts

Abstract Gorlin Syndrome (GS) is a rare condition with multisystemic manifestations. Known features include basal cell carcinomas, odontogenic keratocysts (OKCs), and skeletal abnormalities. Multidisciplinary involvement paramount surgical intervention as common treatment modality. Multiple OKCs recurrence in GS. However, limited up-to-date guidelines are available on the appropriate radiographic monitoring of such lesions, form orthopantomogram, these patients. This case 12-year-old girl GS multiple episodes OKCs. She monitored regularly Oral Maxillofacial team since age 3, after her dentist referred due to its association A multidisciplinary approach Dermatology, Pediatrics, Ophthalmology, Ear Nose Throat, Orthodontics Restorative Dentistry within dental specialty undertaken manage condition. Yearly clinical reviews mouth radiographs biannually were done, first episode presenting at 10 years old. Orthopantomogram magnetic resonance imaging revealed 6 – 2 maxilla, 4 mandible. These surgically enucleated liquid nitrogen cryotherapy adjunct, alongside extractions associated deciduous teeth. Eighteen months following this, OPG showed new 1 removed successfully similar fashion active ongoing. underscores importance regular follow-ups frequency Long-term this syndrome also paramount.